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Description
Clin Exp Neurol 1983, 19: 192-197

L-carnitina un integratore alimentare e dietetico

In OTC deficiency, citrulline is low or normal and urinary orotic acid is increased.3,16 N -Acetylglutamate synthetase (NAGS) deficiency NAGS deficiency is an autosomal-recessive disorder
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It is necessary to maintain a varied and balanced diet and a healthy lifestyle
